| Title | Myocardial fibrosis in desmin-related hypertrophic cardiomyopathy |
| Authors | He, Yi Zhang, Zhaoqi Hong, Daojun Dai, Qinyi Jiang, Tengyong |
| Affiliation | Capital Med Univ, Dept Radiol, Beijing Anzhen Hosp, Beijing, Peoples R China. Peking Univ, Hosp 1, Dept Neurol, Beijing 100034, Peoples R China. Capital Med Univ, Dept Cardiol, Beijing Anzhen Hosp, Beijing, Peoples R China. Capital Med Univ, Dept Radiol, Beijing Anzhen Hosp, 2 Anzhen Rd, Beijing, Peoples R China. |
| Keywords | INTERMEDIATE-FILAMENTS PRIMARY DESMINOPATHIES SKELETAL MYOPATHY MUTATIONS |
| Issue Date | 2010 |
| Publisher | journal of cardiovascular magnetic resonance |
| Citation | JOURNAL OF CARDIOVASCULAR MAGNETIC RESONANCE.2010,12. |
| Abstract | Desmin-related myopathy (DRM) is known to cause different types of cardiomyopathy. Late gadolinium enhancement cardiovascular magnetic resonance (CMR) has been shown to identify fibrosis in ischemic and non-ischemic cardiomyopathies. We present a rare case of desmin-related hypertrophic cardiomyopathy, CMR revealed fibrosis in the lateral wall of the left ventricle. CMR is superior to conventional echocardiography for the detection of myocardial fibrosis in desmin-related cardiomyopathy, which may be useful to detect early cardiac involvement and predict the patient prognosis. |
| URI | http://hdl.handle.net/20.500.11897/241705 |
| ISSN | 1097-6647 |
| DOI | 10.1186/1532-429X-12-68 |
| Indexed | SCI(E) |
| Appears in Collections: | 第一医院 |
